Usher Syndrome

Usher syndrome (sometimes referred to as "Usher's syndrome") is a genetic disease causing deaf-blindness. It is essentially progressive retinitis pigmentosa combined with congenital hearing impairment. It is inherited in an autosomal recessive pattern. While this is a rare genetic condition, it represents the major cause of syndromic deafness with blindness.
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Usher syndrome An AR condition characterized by retinitis pigmentosa–RP and sensorineural deafness [more]Usher syndrome - Community and Resources